特发性右心房扩张症1例

Idiopathic right atrial dilatation:case report

本文报道1例特发性右心房扩张症,患者中年男性,慢性病程,因“发现心动过缓20余年,腹胀1周”就诊于北京大学第三医院心血管内科,超声心动图示:右心房、右心室明显增大,三尖瓣脱垂伴反流(重度),左心房增大,左心室略大,左室壁运动略减低,左室射血分数50%,行三尖瓣置换+右心房减容术+心外膜永久起搏器安置术,术后三尖瓣及右心房病理回报部分区域黏液样变性,术后复查超声心动图示左心房、左心室、右心房增大,二尖瓣反流(轻度),左室射血分数67%。

We reported a case of idiopathic right atrial dilatation.A middle-aged male with a chronic course of disease,was admitted to the Department of Cardiology of Peking University Third Hospital due to"bradycardia for more than 20 years and abdominal distension for 1 week".Echocardiography showed significantly enlarged right atrium and right ventricle,tricuspid valve prolapse with severe regurgitation,and enlarged left atrium and left ventricle,with left ventricular ejection fraction(LVEF)of 50%.The patient underwent tricuspid valve replacement,right atrium volume reduction and permanent epicardial pacemaker placement.Pathological findings of the tricuspid valve and right atrium showed partial mucoid degeneration.Postoperative echocardiography showed enlargement of left atrium,left ventricle and right atrium,mitral regurgitation(mild),and LVEF of 67%.