头颈部恶性血管外皮瘤

Malignant hemangiopericytoma in head and neck region

目的探讨头颈部恶性血管外皮瘤的诊断和治疗.方法对8例术后病理确诊的头颈部恶性血管外皮瘤的临床资料进行回顾性分析.结果8例中男3例,女5例,年龄21～6 5岁.病灶位于颈部、颧部、腮腺、翼腭凹、颞下凹、颏下三角各1例,舌根2例.全部病例采用根治性手术切除.随访5～1 0年,复发3例,双侧颈淋巴结转移1例,2例接受2次手术,1例接受3次手术,死亡1例.结论组织病理学检查是恶性血管外皮瘤的唯一可靠的诊断方法,根治性外科切除手术是主要治疗手段.

Objective To study the diagnosis and treatment of malignant hemangiopericytoma in head and neck region. Methods The clinical data of 8 patients with malignant hemangiopericytoma in head and neck region were analyzed retrospectively. Results Of 8 patients, 3 were male and 5 were female.The age ranged from 21 to 65 years. There were 1 case with lesion located in cervical part , 1 in zygomatic region, 1 in parotid gland, 1 in fossa pterygopalatina, 1 in fossa infratemporalis, 1 in submental triangle, and 2 in root of tongue. All 8 patients underwent radical resection. Local recurrence was found in 3 cases. Two cases received operation twice and 1 case received operation three times. Metastasis was found in bilateral lymph node of 1 case. One patient died on postoperative sixth year. Conclusion The histopathological examination was the only reliable diagnostic method for malignant hemangiopericytoma. The radical resection was still the main measure of treatment for malignant hemangiopericytoma.