眼-脑-肾综合征治疗的回顾性分析(附4例报告)

A RETROSPECTIVE ANALYSIS OF MANAGEMENT RESULTS OF OCULOCEREBRORENAL SYNDROME (A REPORT OF 4 CASES)

目的 :阐述 4例 (8眼 )眼 脑 肾综合征伴有双侧白内障患者的治疗。方法 :回顾性评论。结果 :2例眼 脑 肾综合征患者首次眼科检查时 ,有肉眼可见双侧白内障 ,所有患者都进行了双眼白内障手术。白内障 (8眼 )摘除时平均年龄是 1 5 (1～ 4 )个月。青光眼的诊断和治疗差别较大。诊断青光眼 (7眼 )时的平均年龄是 33 7(1 0 0～ 70 0 )个月。所有眼都进行了随访 ,随访时间平均 5 1 2 (4 2～ 1 90 )个月。结论 :眼 脑 肾综合征患者应及早鉴别并手术摘除白内障 ;必须严密观察病人眼内压、眼底和屈光度的变化 。

Objective:To analyze the management results in 4 patients with oculocerebrorenal syndrome Method:Retrospective review Results:Two cases of oculocerebrorenal syndrome had visually bilateral cataracts on their first full ophthalmic examination All underwent bilateral cataract surgery The mean age (of 8 eyes) at extraction was 1 5(1～4) months The mean age (of 7 eyes) at glaucoma diagnosis was 33 7 (10～70) months All eyes were followed up for an average of 51 2 months Conclusions:Early identification and surgical removal of cataracts is recommended in patients with oculocerebrorenal syndrome Patients should be monitored closely and regularly for changes in intraocular pressure,optic nerve cupping,and refractive error to rule out the development of glaucoma