手术矫治Poland综合征

SURGICAL CORRECTION OF POLAND'S SYNDROME IN CHILDREN

目的 探讨手术矫治 Poland综合征的方法。 方法 1990年 5月～ 2 0 0 2年 5月 ,对 3例年龄分别为3、12和 16岁的女性 Poland综合征患儿进行了胸壁成形术矫治 ,患儿均有胸大肌缺如、胸小肌发育不良及肋软骨缺损等畸形。其中 1例行自身肋软骨移植、右侧背阔肌移位术 ,另 2例行自身肋软骨移植、涤纶布片修补术。 结果 术后分别随访 1、7和 10年 ,结果显示患儿胸壁外观恢复满意 ,患侧上肢及胸背部功能正常 ,生长发育无异常。 结论 Poland综合征是一组涉及多部位的先天畸形 ,应根据病变的程度和范围制定手术治疗计划 。

Objective To introduce a method of the surgical correction of Poland's syndrome in children. Methods From May 1990 to May 2002, 3 female children with Poland's syndrome were treated. One child of 12 years old with defects of the right second and third costal cartilages, pectoralis major and pectoralis minor underwent repair of chest wall with graft of autologous costal cartilage from left sixth costal cartilage and transfer of the latissimus dorsi flap. The other 2 children, 3 and 16 years old, with defects of the left second, third and fourth costal cartilages, pectoralis major and pectoralis minor underwent graft of autogenous costal cartilage from the right sixth costal cartilage and implant of Dexon mesh. Results Three patients were followed up 1, 7 and 10 years postoperatively, respectively.The contour of chest wall in 3 patients were improved. The functions of the chest, back and upper limbs in the deformitis side were good and the growth and development of the children were normal during follow-up postoperatively.Conclusion The congenital deformities of multiple systems and parts in the body are involved in Poland's syndrome so that it is necessary to make a proper surgical plan according to the extent of lesions for a satisfactory result.