小儿先天性肝囊肿

Congenital Hepatic-cysts in Children

目的探讨小儿先天性肝囊肿的临床表现、诊断及鉴别诊断,正确选择治疗方法。方法回顾性研究我院自1972年至今的14例小儿先天性肝囊肿病例,评价其治疗手段。结果本组14例均行手术治疗,其中6例多囊肝病例中,1例术后呼吸衰竭死亡。8例孤立性肝囊肿中,2例行开窗引流,5例行不同形式的肝切除手术,1例行囊肿空肠Roux—Y吻合术。除3例多囊肝病例术后仍有轻度肝肿大外,其余患儿预后良好。结论小儿先天性肝囊肿的治疗,应根据其不同表现,采取不同治疗手段,以达到满意疗效。

Objective To explore the clinical characteristics, diagnosis and differential diagnosis of the congenital cyst of liver in children and to select the reasonable treatment. Methods Retrospective study was carried out in the fourteen children with congenital cyst of liver in our hospital since 1972 , in order to evaluate the treatment. Results All these fourteen cases were treated using operation. One of the six cases with multiple hepatic-cyst died of respiratory failure during post-operation. Two cases drainage were performed by fenestration. Five were performed using different hepatectomy and the last one was performed cyst-jejunum Roux-Y anastomosis. All the children were in good health, except that mild hepatomegaly occurred in three multiple hepatic-cyst cases after surgical treatment. Conclusions The different treatment of congenital hepatic-cyst in children depends upon different clinical characteristics. Doing so, satisfactory therapeutic effect for hepatic-cost could be obtained.