肺淋巴管平滑肌瘤病影像学特征及误诊分析鄢

Imaging study and misdiagnosis of pulmonary lymphangioleiomyomatosis

目的探讨肺淋巴管平滑肌瘤病的影像表现及误诊原因。方法收集3例经病理证实的PLAM的X线、CT片,由三名医生共同分析影像表现及临床资料,并结合文献复习。结果3例均为育龄期妇女,影像主要表现为肺部弥漫性网状、囊状改变;均长期误诊为慢性支气管炎、支气管扩张、肺间质纤维化。结论PLAM在高分辨率CT(HRCT)下具有特征性,在熟悉该病的影像表现基础上结合临床表现全面分析,可减少误诊。

Objective: To research the imaging features of Pulmonary Lymphangioleiomyomatosis (PLAM).Methods: Three cases of chest film and CT were confirmed by pathology,the imaging materials and clinical data were analysed, along with a review of the related literature by three radiologists. Results: The three cases were women of childbearing ages, Imaging appearance is extensive honeycomb and cystic airspace patter. They were all diagnosed as chronic bronchitis, bronchiectasis and interstitial pulmonary fibrosis for a long time. Conclusion: HRCT is sensitive to PLAM. In order to reduce misdiagnosis of PLAM, we must master imaging appearance of the disease combined with the clinical data to make a comprehensive diagnosis on the main imaging features.