原发性肺动脉高压的诊断（附3例临床及病理分析）

Diagnosis of Primary Pulmonary Hypertension──Clinicopathologic Analysis of Three Cases

作者对本院４０年来在６９３５例尸检中发现的原发性肺动脉高压（ＰＰＨ）３例，进行临床及病理分析，并结合文献复习着重讨论了ＰＰＨ的诊断。本组３例其诊断要点为：①典型的临床表现，特别是活动性呼吸困难和晕厥；②影像检查有肺动脉扩大，主动脉相对缩小，肺纹纤细、肺动脉高压及右心室肥大等；③尸检，以Ｈｅａｔｈ分级Ⅳ～Ⅴ级的肺血管改变为主的病变。

Three cases of primary pulmonary hy-pertension (PPH) were found in 6935 autopsies withinthe past 40 years at the universkity hospital. Compara-tive study of clinical and Pathologic data were also Per-formed.The authors revied the literature con-cerned, and discussed the diagnosis and misdiagnosisof PPH.