特发性肺含铁血黄素沉着症临床X线表现

The clinical and X-ray Diagnosis of Idiopathic Pulmonary Hemosiderosis

目的:探讨肺含铁血黄素沉着症临床X线诊断。方法:27例均有完整的临床、实验室及胸片,均经病理证实。结果:17例肺弥漫分布有片絮状或磨玻璃样阴影,6例有结节状、粟粒状阴影,4例弥漫分布网织状阴影。结论:胸片是发现并提示肺含铁血黄素沉着症的最基本检查方法,与临床相结合,尤其是痰或胃液中查到含铁血黄素巨噬细胞,可明确诊断。

Objective To study the X-ray and clinical diagnosis of Idiopathic Pulmonary Hemosiderosis.Methods This study included 27 cases with pathologically proved IPH,all patients had complete clinical and laboratory data as well as chest films。 Their X-ray findings were retrospectively analyzed.Results diffuse flake consolidation and ground-glass shadows(n=17),diffuse military and micronodular shadows(n=6),and diffuse reticular shadows(n=4) were demonstrated in both lungs.Conclusions Plain radiography is the elementaryg means to detect this disease ,combined with clinical data, particularly the presence of hemosiderin macrophagocyte in the sputum,gastric juice can confirm the diagnosis.