先天性虹膜基质囊肿

Congenital iris stroma cysts

目的 阐述先天性虹膜基质囊肿的临床特点、病理组织学特点以及有效的治疗方法。方法 对我院 1 979年～ 2 0 0 3年诊治的 8例先天性虹膜基质囊肿的临床资料进行回顾性分析。结果 7例为婴幼儿或青少年 ( 5个月～ 1 9岁 ) ,1例为 4 8岁成年人。确诊年龄 :6例在 1岁前确诊 ,2例分别为 1 0岁和 2 0岁。女 7例 ,男 1例。左眼 7例 ,右眼 1例。位置 :虹膜下方 5例 ,虹膜颞侧 1例 ,累及全部虹膜 2例。 5例术前眼压高 ( 2 6～ 6 4mmHg)。 8例均有角膜混浊、变性。 3例晶状体混浊。本组 7例均采用囊肿抽吸联合扇形或全部虹膜囊肿切除 ,术后无复发。 1例眼球摘除。结论 先天性虹膜基质囊肿主要发生于婴幼儿。早期采用囊肿抽吸联合包括囊肿在内的扇形或全部虹膜切除是最有效的治疗方法。

Objective To describe clinical characteristics,management,and complications of congenital iris stroma cysts.Methods Retrospective study on the medical records of 8 patients(8 eyes)with congenital iris stroma cysts from 1979 to 2003.Results 7patients were chidren or teenagers(range,5months～19 years),6 of which were diagnosed under age 1 year,and 1 were age 10 years;1 patient was adults and was diagnosed in 20 years.lris stroma cyst was more common in girls,and left eyes,and more located in the inferior aspect of the iris.In 5 children,the cyst caused glaucoma.In all cases were used techniques of aspiration and surgical excision,none recurred.Conclusions Congenital iris stoma cysts are uncommon and usually occur in infancy,which require early treatement by aspiration and surgical excision as soon as possible.