肺泡蛋白沉积症的CT表现

CT features of pulmonary alveolar proteinosis

目的 :探讨肺泡蛋白沉积症的CT表现。方法 :回顾性分析了 6例肺泡蛋白沉积症患者的CT资料 ,其中男性 4例 ,女性 2例 ,平均年龄 38.5岁。结果 :6例均表现为双肺广泛的肺浸润阴影 ,边界清晰 ,呈地图样变 ,其中 4例肺野呈磨玻璃样改变 ,3例可见支气管充气征 ,2例累及肺尖 ,2例分布在为外周。结论 :尽管肺泡蛋白沉积症少见 ,但CT表现有其特征性。再结合临床综合分析 ,诊断并不困难。

Objective:To study CT features of pulmonary alveolar proteinosis(PAP).Methods:CT manifestations of PAP in 6 cases were studied retrospectively. 4 were male and 2 were female, and the average age is 38.5 years old.Results:There were diffused patchy cloudy shadows with sharply defined margins and geographical appearances of two lungs in all cases. Ground glass shadows in 4 cases. Air-brchogram sign in 3 cases distributed arround the lung in 2 cases.Conclusion:Although PAP is rare, there are characteristic features of CT for PAP, referring to the clinical history and we can made a reliable diagnosis.