肺淋巴管肌瘤病的HRCT表现

CT Findings of Pulmonar Lymphangioleimymatosis

目的探讨肺淋巴管平滑肌瘤病(PLAM)HRCT表现,提高对该病的诊断水平。方法1例经肺活检病理证实的肺淋巴管平滑肌瘤病患者,行胸部CT平扫和HRCT检查。回顾性分析其临床特征及HRCT表现。结果该例为育龄期女性,其HRCT特征性表现为:双肺弥漫分布大小不一囊状透光区,囊腔直径2～15mm,多数为10mm左右。结论PLAM的HRCT表现具有特征性,结合临床特征可提示该病的诊断。

Objective To investigate the CT findings of pulmonary Lymphangioleimymatosis, and to improve the diagnosis ability of the disease. Methods One case of pulmonary Lymphangioleimymatosis proved by surgery and pathology, underwent chest CT and HRCT scanning. Both clinical characteristics and HRCT findings were analyzed retrospectively. Results This patient is Women in child-bearing age. Characteristic HRCT findings in patients with PLAM, included multiple well-defined cystic air spaces surrounded by uniformly thin walls, its diameter from 2 to 15mm and most of them were 10mm. Pulmonary cysts distributed diffusely throughout both lungs. Conclusion HRCT findings of pulmonary lymphangioleiomyomatosis are characteristics and HRCT is the imaging method to display PLAM. The Characteristic HRCT findings combined with the clinical feature are very suggestive for making a diagnosis.