骨纤维异常增殖症（附120例报告）

Fihrous Dysplasia of Bone ( An Analysis of 120 Cases)

笔者报告了１２０例经病理证实的骨纤维异常增殖症（简称骨纤）。其中单骨型９８例（占８１．７％），多骨型２２例（占１８．３％），后者包括５例Ａｌｂｒｉｇｈｔ综合征。从Ｘ线表现上可分为囊肿型（８３灶）、弥漫型（１４０灶）、丝瓜瓤型（８灶）、虫噬型（３灶）和纤维骨瘤样改变（４灶）五种类型。四肢长骨６３例病变的Ｘ线病理观察发现胚骨和其他四肢长骨病灶内的骨小梁周围均有程度不同的成骨细胞镶边和骨小梁周边的板层转化现象，两者的出现率无明显差异（Ｐ＞０．０５）。笔者重点讨论了骨纤和骨化性纤维瘤的异同，发现两者尤其在病理上没有原则的区别，因而认为所谓的骨化性纤维瘤就是骨纤。

In this paper, 1 20 cases of pathologically proved fibrous dysplasia of bone were re-ported. of which 98 were of monostotic type(81.7%),and 22 cases(18。3%)polystotic type including 5cases of Albright’s syndrome. Roentgenologically, they were divisible into 5 types;cystic type(83 cases),diffuse type(140 cases),sponge groud-flesh type(8 cases),moth-eaten type(3 cases) and fibrous osteomatoid change(4 cases). The lesions of 63 cases of long bone were examined roentgenolog-ically and pathologially. It was found that some woven bone trabeculae of the lesions in the tibia and other long bones were rimmed with osteoblasts and lamellar transformation at their periphery. The inci-dence of the two signs did not show significant statistical difference(P> 0.05).The differences be-tween fibrous dysplasia and ossifying fibroma of bone were discussed.The authors considered there is no essential difference,between the two conditions(in the pathological features especially).So that they might be taken to be the sa me disease ent ity.