45例先天性内耳畸形的高分辨率CT特征

HRCT imaging charaterized of congenital abnormalities of the inner ear in 45 cases

目的 :探讨先天性内耳畸形的高分辨率CT(HRCT)特征及其在先天性内耳畸形诊治中的意义。方法 :总结 4 5例先天性内耳畸形的临床资料 ,分析颞骨HRCT所见。结果 :4 5例耳聋多起于幼儿 ,呈缓慢进行性感音神经性听力减退 ,波动性者 15耳 ;17耳半规管麻痹。HRCT显示 :Michel型 3例 (4耳 ) ;Mondini型 2 5例 (39耳 ) ;不伴内耳畸形的前庭水管扩大 13例 (2 3耳 ) ;内耳道发育畸形 4例 (5耳 )。伴中、外耳畸形 13耳。结论 :HRCT对先天性内耳畸形具有重要的诊断价值 ,并为临床治疗。

Objective:To explore the high resolution CT (HRCT) image charaterized of congenital abnormalities of the inner ear(CAIE),and its value in the diagnosis and treatment of CAIE. Method:The clinic data and axial HRCT scans of CAIE in 45 cases were analyzed. Result:In 45 CAIE patients, most of them were frequently associated with slowly progressive sensorineural hearing loss in childhood, 15 ears were fluctuating hearing loss. Seventeen ears were unilateral semicircular canal paralysis. HRCT showed that Michel type 3 cases(4 ears), Mondini type 25 cases(39 ears). Large vestibular aqueduct malformation not associated with anomalies of inner ears 13 cases(23 ears), anomalies of internal auditory canal 4 cases (5 ears). Thirteen ears were associated with outer and middle ear malformation.Conclusion: HRCT image has the important value in the diagnosis and treatment of CAIE,especially for the excerpt of indication of cochlear implantation.