先天性肺发育不全3例报道及文献复习

Congenital pulmonary hypoplasia:a report of 3 cases and review of literature

目的 探讨先天性肺发育不全的临床特征。方法 用回顾性方法分析先天性肺发育不全 3例并文献复习。结果 先天性肺发育不全的原因可能与遗传、胚胎早期病毒感染等因素有关。通过 X线、纤维支气管镜、 CT检查及外科手术可确诊。结论先天性肺发育不全是一种少见病，病人易继发肺部感染，因此对反复呼吸系统感染的青少年要注意本病的可能。

Objective To investigate the clinical character of congenital pulmonary hypoplasia. Methods Three cases of confirmed congenital pulmonary hypoplasia were retrospectively analyzed and some literatures about this disease were reiewed.Results The cause of congenital pulmonary hypoplasia may be related with heredity and virus infection early on fetus. This disease may be confirmed by x－ rays、 fibroptic bronchoscopy、 CT and surgery therapy. Conclusion Congenital pulmonary hypoplasia is a rare disease. If young patients suffered from pulmonary infection repeatly, congenital pulmonary hypoplasia should be considered.