先天性心脏病合并永存左上腔静脉及右上腔静脉缺如畸形的九例报告

ABSENT RIGHT SUPERIOR VENA CAVA WITH PERSISTENT LEFT SUPERIOR VENA CAVA

本文报道了在施行先天性心脏病心内直视手术中，发现永存左上腔静脉合并右上腔静脉缺如９例。其中法乐四联症、室间隔缺损各３例；房间隔缺损、右室双出口、单心室一单心房各１例。手术死亡２例。本文对永存左上腔静脉合并右上腔静脉缺如的诊断、术中左上腔静脉的处理、心律的变化特点及其预防与诊治，进行了讨论。

Among 326 patients of persistent left superior vena cava (PLSVC) , 9 were found to have associated with absence of right superior vena cava(RSVC) during intracardiac operation. 2 of them died after operation. Because of the rarity of this congenital anomaly (0. 47/000)the clinical and surgical implications were discussed.