Moyamoya病的临床表现与影像学特征研究(附31例报告)

An observation on the clinical manifestation and imaging characteristics in 31 patients with Moyamoya disease

目的总结Moyamoya病的临床表现及影像学特征。方法回顾性分析我院1992年2月至2004年10月经DSA或MRA确诊的31例Moyamoya病患者的临床及影像学资料。结果31例患者平均年龄25·7岁;脑卒中和头痛是本组Moyamoya病患者最常见的临床表现,发生率分别为83·9%(26例)和74·2%(23例);儿童及青少年患者以缺血性脑卒中发病为主,而成年患者以出血性脑卒中发病为主;所有患者均有颈内动脉或其分支狭窄或闭塞和Moyamoya血管形成,其中有27例患者的CT或MRI表现为双侧病灶。结论对于年轻无脑血管病危险因素的一时性缺血性发作(TIA)或脑卒中患者,尤其有卒中史或反复头痛发作者必须使用MRA以除外Moyamoya病。

Objective To investigate the clinical manifestation and imaging characteristics of Moyamoya disease. Methods Clinical and imaging data of 31 patients with Moyamoya diease in our hospltal,from Feb. 1992 to Oct,2004, were analyzed retrospectively. Results The mean age of the 31 patients was 25.7. The main clinical manifestations were stroke and headache, the frequency of stroke was 83.9% （26/31） , headache was 74. 2% （23/31） ,in juvenile cases the ischemic stroke was the salient clinical feature,but the hemorrhagic stroke in adult. The internal carotid arteries or their branches of the patients showed stenosis or occlusion,and nearby the basicranial vascular occlusion,the vascular network, namely Moyamoya vascular,was visualized. Conclusion While the young patient without the cerebrovascular risk factor was suspected of transient ischemic atlack or stroke,we should except the Moyamoya disease with the aid of MRA, especially they were possessed of stroke history or recurrent headache.