新生儿脐膨出的早期修复

EARLY REPAIR OF OMPHALOCELE ON NEONATES

１９８８年６月～１９９４年１２月，对１０例新生儿脐膨出进行了诊治。其中９例经早期手术修补得到治愈。经３个月～５年随访，患儿生长发育良好。强调早期手术修复的重要性，并对手术方法的选择。

Omphalocele is a less common congenital malformation in neonates and belongs to the realm of emergent surgical treatment. Early repair is of crucial importance for saving the patients life. Ten neonates with omphalocele have undergone early surgical repair since 1988. The overall result was satisfactory. There were 8 boys and 2 girls. The time of operation ranged from one to forty eight hours after birth (24 hours in 8 cases). All of them were term neonates, except in one case being premature. None of them had rupture of the sac membrane. The minor and major omphalocele were in 8 and 2 cases, respectively. Five cases accompanied with other congenital malformations (1 to 3 kinds). One case of them was complicated by exompholos macroglossia gigantism (EMG syndrome). Nine cases were treated by primary stage of surgical repair. One case with major omphalocele had undergone two staged operation. Nine neonates were survived and only one died of pneumonia and scleroderma postoperatively. The patients were followed up for 3 months to 5 years, 9 cases were satisfactory. Early surgical repair was essential to successful treatment. The choice of surgical methods, the management of concomittant malformation in the alimentary tract and the factors influencing the prognosis were discussed.