特殊的儿童嗜铬细胞瘤4例报告

Rare types of pheochromocytoma in children: A report of 4 cases

目的探讨小儿特殊嗜铬细胞瘤的临床特点及治疗。方法报告2000-2004年间我院收治的4例小儿嗜铬细胞瘤病例，均为男性，年龄9～12岁。其中双侧肾上腺嗜铬细胞瘤2例，肾上腺外3例，异时再发者2例，有家族史1例。结果经妥善围手术期处理，顺利切除肿瘤，术后血压全部降至正常。结论儿童肾上腺外、双侧肾上腺．多发及再发的嗜铬细胞瘤发生率高于成人，手术切除肿瘤可获得良好的治疗效果。

Objective To evaluate the clinical characteristics and treatment of rare types of pheochromocytoma in children. Methods The clinical data from 4 boys （aged from 9 to 12 years） with rare types of pheochromocytoma were retrospectively analyzed. Two cases suffered from bilateral adrenal tumor, 3 with extra-adrenal tumor, 2 with metachronous recurrence, and the other one with familial occurrence. Results All the patients underwent operation with the help of proper peri-operative management. The pheochromocytomas were completely removed. Patients＇ blood pressure returned to the normal after operation. Conclusions More extra-adrenal, bilateral adrenal and metachronous recurrent pheochromocytomas can be found in children. The satisfactory results can be gained if tumor can be totally removed.