摘要
腹膜后纤维变性是纤维组织的稠密的匾的形成在制动火箭腹膜描绘的不平常的混乱,并且它的病原学仍然保持未知。自体免疫的胰腺炎是纤维变性在胰与 IgG4 积极的血浆房间和淋巴细胞和 obliterative 静脉炎的丰富的渗入描绘的慢性胰炎的一种稀罕类型。我们在场在制动火箭的出现以后开发了 10 瞬间的自体免疫的胰腺炎的一个盒子腹纤维变性。resected 制动火箭腹团的组织检查所见是有 IgG4 积极的血浆房间和淋巴细胞和 obliterative 静脉炎的丰富的渗入的显著 periureteral 纤维变性。这些调查结果在这种情况中为制动火箭腹纤维变性和自体免疫的胰腺炎建议普通 pathophysiological 机制。制动火箭腹纤维变性力量的一些盒子是 IgG4 相关的致硬化的疾病的制动火箭腹损害。
Retroperitoneal fibrosis is an uncommon disorder characterized by the formation of a dense plaque of fibrous tissue in the retroperitoneum, and its etiology remains unknown. Autoimmune pancreatitis is a rare type of chronic pancreatitis characterized by fibrosis with abundant infiltration of IgG4-positive plasma cells and lymphocytes and obliterative phlebitis in the pancreas. We present a case of autoimmune pancreatitis that developed 10 mo after the occurrence of retroperitoneal fibrosis. Histological findings of the resected retroperitoneal mass were marked periureteral fibrosis with abundant infiltration of IgG4-positive plasma cells and lymphocytes and obliterative phlebitis. These findings suggest a common pathophysiological mechanism for retroperitoneal fibrosis and autoimmune pancreatitis in this case. Some cases of retroperitoneal fibrosis might be a retroperitoneal lesion of IgG4-related sderosing disease.