摘要
紫癜 hepatis 是肝窦状隙和充满血的空格的膨胀在主要在暴露于有毒的物质或雌激素的题目观察的肝描绘的一个稀罕条件，它经常是无征状的。仅仅当门静脉高血压的出血性的复杂并发症发生时，非肝脏硬化症的自发的门静脉高血压(NCIPH ) 也是很少在欧洲国家观察的肝的脉管的疾病，它通常被诊断。我们在与肝紫癜被诊断的年轻白种人男性报导 NCIPH 的一个案例，显示出 ultrasonographic 和门静脉高血压四年的内视镜的符号在以后。第二活体检视为 NCIPH 是诊断的。就算致病仍然保持阴暗，紫癜 hepatis 能被看作肝的脉管的疾病的一个早符号，它可以进行到更明确的条件。
Peliosis hepatis is a rare condition characterized by dilatation of hepatic sinusoids and blood-filled spaces in the liver mainly observed in subjects exposed to toxic substances or estrogens, which is frequently asymptomatic. Non-cirrhotic idiopathic portal hypertension （NCIPH） is also a vascular disease of the liver rarely observed in European countries, which is usually diagnosed only when the hemorrhagic complications of portal hypertension occur. We report a case of NCIPH in a young Caucasian male who was diagnosed with liver peliosis, showing ultrasonographic and endoscopic signs of portal hypertension four years after. A second biopsy was diagnostic for NCIPH. Even if the pathogenesis remains obscure, peliosis hepatis can be considered as an early sign of vascular disease of the liver, which may progress to more definite conditions.
基金
a grant on Vascular Disorders of the Liver from Dipartimento di Medicina Interna, Cardioangiologia, Epatologia, Universita di Bologna to Dr. A Berzigotti
关键词
紫癜
高血压
静脉
病理机制
Peliosis hepatis
Idiopathic portal hypertension
Hepatic veins catheterisation
