镰刀综合征外科治疗的临床分析

Analysis of the Surgical Treatment of Scimitar Syndrome

目的 探讨镰刀综合征外科治疗方法的选择。方法 回顾分析我院1999年1月～2004年7月12例镰刀综合征患者的临床资料，10例采用经典房内通道技术；1例采用体外循环，用人工血管将镰刀静脉与左心房相连；1例在非体外循环下直接将镰刀静脉吻合在左心房。结果 12例患者无手术及远期死亡，均无需二次手术。随访1～36个月，所有患者恢复良好，超声心动图显示未见明显的肺静脉回流梗阻。结论 治疗镰刀综合征的手术方法应根据术中异位回流肺静脉的具体位置决定，恰当的方法均可起到良好的手术效果。

Objective To investigate how to choose the methods of surgical treatment for Scimitar syndrome. Methods From Jan. 1999 to July 2004, the clinical data of 12 patients with Scimitar syndrome were analyzed retrospectively, 10 patients underwent repair by intra-atrial baffles approach, one patient by connecting scimitar vein and left atrium with artificial blood vessel under cardiopulmonary bypass, and one patient by directly reimplanting the scimitar vein to left atrium without cardiopulmonary bypass. Results All the 12 patients had no perioperative or late deaths and none of them required reoperation. Follow-up was extended from 1 to 36 months, echocardiography demonstrated a patent anastomosis in all patients without any evidence of restenosis. Conclusions Surgical approaches to Scimitar syndrome is based on the anatomic and pathologic features presented in each case. Approriate method will have good result.