改建右室流出道一肺动脉姑息治疗小儿重症法乐四联症

Palliative Management of Severe Tetralogy of Fallot by Right Ventricular Outflow Tract-pulmonary Artery Reconstruction

为探讨一种更好的小儿重症法乐四联症姑息手术方法，１９８４年１０月至１９９４年１２月在体外循环下应用右室流出道一肺动脉改建术治疗１８例重症法乐四联症病儿，平均年龄５．３岁，平均体重１４ｋｇ。结果住院死亡１例（５．５％）。随访２个月～３年，平均随访１．５年，病儿青紫改善、左室及肺血管均发育良好。作者认为改建右室流出道一肺动脉是姑息治疗小儿重症法乐四联症的有效方法之一。

Eighteen pediatric patients with severe tetralogy of Fallot underwent palliative right ventricular out flow tract-pulmonary artery reconstruction,using cardiopulmonary bypass from October,1984 to December,1994.In this group of patients,there were 12 boys and 6 girls with an average age of 5.3 years and an average body weight of 14kg. Hospital mortality was 5.5%(1/18).Marked improvement of cyanosis and progressive enlargement of the hypoplastic pulmonary arteries were found during a follow-up of a mean 1.5 years.The clinical results indicate that the technique employed is one of the good palliative operations for severe tetralogy of Fallot.