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8p11骨髓增殖综合征——一例报告及文献复习 被引量:10

8p11myeloproliferativesyndrome onecasereportandliteraturereview
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摘要 为提高对骨髓增殖综合征的认识,报告1例8p11骨髓增殖综合征,进行文献复习。其特征是骨髓粒系高度增生,嗜酸粒细胞增多,淋巴结肿大和高危发生T细胞非霍奇金淋巴瘤及演变为急性髓系白血病。染色体核型异常累及8p11。 Apatientwith8p11myeloproliferativesyndromecharacterizedbymyeloidhyperplasia,eosinophilia,andlymphadenopathywasreported,andtherelatedliteraturewasreviewed.
机构地区 中国医学科学院
出处 《中华血液学杂志》 CAS CSCD 北大核心 1996年第11期566-568,共3页 Chinese Journal of Hematology
关键词 骨髓增生病 染色体核异常 t(8 13)Myeloproliferativedisorders
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  • 1赵喜晨,王建祥.8p11骨髓增殖综合征的研究进展[J].国外医学(输血及血液学分册),2005,28(3):212-215. 被引量:5
  • 2鲁道远,崔为发,李知森,徐衍明,傅梅林,刘希光,王云.恶性实体瘤与白血病迭合10例[J].中华血液学杂志,1995,16(5):258-259. 被引量:5
  • 3石奇珍,吕联煌,梁玉英,黄淑桦,战榕.慢性粒细胞白血病并发恶性淋巴瘤(附7例分析)[J].中国肿瘤临床与康复,1996,3(4):56-57. 被引量:3
  • 4Swerdlow SH, Campo E, Hanis NL, et al. WHO classification of tumors of haematopoietic and lymphoid tissues. 4th ed. Lyon : International Agency for Research Cancer Press,2008: 74-75.
  • 5Macdonald D, Aguiar RC, Mason PJ, et al. A new myeloproliferatire disorder associated with chromosomal translocations involving 8p11 : a review. Leukemia, 1995, 9 : 1628-1630.
  • 6Friedhoff F, Rajendra B, Moody R,et al. Novel reciprocal translocation between chromosomes 8 and 9 found in a patient with myeloproliferative disorder. Cancer Genct Cytogenet, 1983, 9:391-394.
  • 7Lewis JP, Jenks H, Lazerson J. Philadelphia chromosome-negative chronic myelogenous leukemia in a chiht with t(8 ;9 ) ( p11 or 12; q34). Am J Pediatr Hematol Oncol, 1983, 5:265-269.
  • 8Abruzzo LV, Jaffe ES, Cotelingam JD,et al. T-cell lymphoblastic lymphoma with eosinophilia associated with subsequent myeloid malignancy. Am J Surg Pathol, 1992, 16:236-245.
  • 9Yamamoto K, Kawano H, Nishikawa S, et al. A biphenotypic transformation of 8p11 myeloproliferafive syndrome with CEP1/ FGFRI fusion gene. Eur J Haematol, 2006, 77:349-354.
  • 10Xiao S, Nalabolu SR, Aster JC, et al. FGFR1 is fused with a novel zinc-finger gene, ZNF198, in the t (8; 13 ) leukaemia/lymphoma syndrome. Nat Genet, 1998, 18:84-87.

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