小婴儿先天性主动脉弓中断合并心内畸形的Ⅰ期手术治疗

One-stage repair of interrupted aortic arch in infants associated with cardiac anomalies

目的总结小婴儿主动脉弓中断合并心内畸形Ⅰ期手术治疗经验。方法2001年9月~2004年8月,手术治疗小婴儿主动脉弓中断合并心内畸形10例。男性7例,女性3例,手术年龄18d^7个月,平均年龄(3.37±2.45)个月,平均体重(5.33±1.72)kg。所有病例术前均有反复呼吸道感染史,病例分型A型7例,B型3例。均采用胸骨正中切口Ⅰ期手术纠治主动脉弓中断和心内畸形。结果全组病例均存活,随访3个月~3年,恢复良好。结论小婴儿主动脉弓中断合并心内畸形采用胸骨正中切口,操作简便,术野暴露清楚,创伤小,有利于术后恢复。由于该病早期发生肺动脉高压,宜尽早手术。

Objective The aim of this study was to review the clinical experience of one-stage repair of interrupted aortic arch （IAA） in infants with cardiac anomaly. Methods Between September 2001 and August 2004, ten patients （7 male, 3 female） with IAA underwent total repair. The average age of patients was 3.37 months （18 days to 7 months） and the mean body weight was （5.33 ± 1.72） kg. All patients had repeated respiratory infection. Seven patients belonged to IAA type A, and three to type B. The operations were performed via midline sternotomy, and the IAA associated with cardiac anomaly was repaired. Results All patients survived and were followed up, with excellent results. Conclusions Midline sternotomy one-stage repair of IAA with associated cardiac anomalies results in good recovery.