摘要
目的:探讨大前庭导水管综合征(LVAS)的诊断、听力学表现及治疗。方法:回顾分析我科2000至2005年9例LVAS的病史、听力学及前庭功能检查、影像学检查及治疗结果。结果:9例均为双耳发病,并呈进行性听力下降,8例纯音测听虽以感音神经性聋为主,但低频段存在一定的气骨导差,保守治疗远期效果不理想。结论:对于儿童不明原因的听力下降,首先应排除先天性疾病,合并其他因素造成的听力下降会增加LVAS诊断的难度。对LVAS进行性听力下降者应尽早选配助听器,并考虑行人工耳蜗植入术。
Objective: To explore the diagnosis, hearing and treatment of large vestibular aqueduct syndrome (LVAS). Method: A retrospective analysis was conducted on the history, auditory and vestibular function, imaging examination, and treatment in 9 cases from 2000 to 2005. Results: All 9 cases presented bilateral large vestibular aqueduct syndrome, and showed progressive hearing loss. Although sensorineural hearing loss was predominant, conductive hearing loss existed in low-tone frequencies in 8 cases. Long-term results of conservative treatment were not ideal. Conclusions: Hearing loss in children with uncertain reasons should be excluded from congenital diseases. Other factors combined can increase difficulties in diagnosis of LVAS. Hearing-aids should be used in patients with progressive hearing loss as early as possible and cochlear implantation should be considered.
出处
《山东大学耳鼻喉眼学报》
CAS
2006年第3期212-214,共3页
Journal of Otolaryngology and Ophthalmology of Shandong University
关键词
大前庭导水管综合征
诊断
耳蜗植入术
Large vestibular aqueduct syndrome
Diagnosis
Cochlear implantation