Komoto综合征

Komoto's syndrome, review of literature

Ｋｏｍｏｔｏ综合征是以先天性上睑下垂，小眼裂，倒向内眦赘皮和内眦间距离增宽为主要特征的临床综合征，以往曾以遗传性睑裂狭小综合征、先天性眼睑内联征报告，目前国内尚无全面反映这一综合征的材料，为此本文总结了在我科治疗的１４例病例并复习了相关的文献。Ｋｏｍｏｔｏ综合征是常染色体显性遗传，而在本组１１／１４无遗传病史，因此提醒我们应对其发病机制作更进一步的研究。应用双“Ｚ”、“Ｚ”成形术、Ｍｕｓｔａｒｄｅ方法及额肌瓣悬吊术，可以使病人得到满意矫治。

Komoto's syndrome comprises epicanthal folds,telecanthus, ptosis and blepharophimosis. It was once called as the congenital eyelid tetrad. As an inheritant disease, it is in-herited in an autosomal dominant fashion. In the past ten years. 14 cases of the komoto's syndrome were treated in our department with Z-plast, mustarde's method and frontalis suspension for epicanthal fold5,telecenthus,and ptosis.The results were satisfactory. In order to gain more informa-tion about the syndrome,some related papers were reviewed. The inheritant characters of the disease were also discussed in the paper