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核纤层蛋白Lamins的结构、功能及相关疾病的研究 被引量:1

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摘要 核纤层蛋白(Lamins)属中等纤维蛋白家族(IF),其多聚体组成网格状结构紧贴于内层核膜内表面,在维持核的正常形态以及在核周期性的解体和重组装过程中发挥重要作用。蛋白内部不同位点的缺失和突变目前已知可引起四种不同的临床综合征。
出处 《中国分子心脏病学杂志》 CAS 2002年第4期57-62,共6页 Molecular Cardiology of China
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