布加综合征诊治现状

Diagnosis and Treatment of Budd-Chiari Syndrome

布加综合征(BCS)的病因目前尚不清楚,部分隔膜型BCS的隔膜可能为下腔静脉血栓吸收机化后所致。目前的各种人工血管转流手术远期疗效不佳,应推广介入治疗和病变的根治性切除术,而过去分型中的下腔静脉狭窄实际是因肝脏增大压迫所致,不应该包括在BCS分型中。

The etiology and pathology of Budd-Chiari syndrome （BCS） remain unclear. The membrahe in some membranous BCS may be derived from the absorption and organization of the thrombus of inferior vena cava （IVC）. The long-term eft＇icacies of currently available graft shunt operations are unsatisfactory. Interventional therapy or radical resection of lesion should be recommended. The IVC stenosis actually results from the compression of hepatomegaly and should not be classified as BCS. The membranous BCS is an acquired disease.