摘要
Airway-centered interstitial fibrosis （ACIF）, a novel .form of diffuse interstitial lung disease （ILD） of unknown cause, was recently presented. There is no final conclusion on its property and denomination, and it might be a new type of idiopathic interstitial pneumonia （IIP）. Histopathologically, it was characterized by progressive lobular or small ACIF, and neither similar to any known category of airway disease and ILD, nor similar to known subtype of HE It showed a poor response to corticosteroids and poor progrnosis. It has been reported in Caucasian patients, here, we utilized the term idiopathic airway-centered interstitial fibrosis （IAIF） for the disease to report 2 Chinese patients, in order to improve understanding and diagnosis of this disease.
Airway-centered interstitial fibrosis （ACIF）, a novel .form of diffuse interstitial lung disease （ILD） of unknown cause, was recently presented. There is no final conclusion on its property and denomination, and it might be a new type of idiopathic interstitial pneumonia （IIP）. Histopathologically, it was characterized by progressive lobular or small ACIF, and neither similar to any known category of airway disease and ILD, nor similar to known subtype of HE It showed a poor response to corticosteroids and poor progrnosis. It has been reported in Caucasian patients, here, we utilized the term idiopathic airway-centered interstitial fibrosis （IAIF） for the disease to report 2 Chinese patients, in order to improve understanding and diagnosis of this disease.
基金
This work was supported by a grant from the Basic Research Programs of Science and Technology Commission Foundation of Shanghai(No.034119868).
