摘要
阵发性睡眠性血红蛋白尿(PNH)是一种少见的克隆性造血干细胞(HSC)疾病,临床主要特点是慢性溶血,易发生静脉血栓和骨髓抑制。临床根据经典PNH或低增生性PNH的不同特点,给予相应的治疗。新近报道的人源化抗C5单克隆抗体eculi- zumab的出现,给PNH患者带来了希望。
出处
《世界临床药物》
CAS
2007年第8期469-471,496,共4页
World Clinical Drug
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