57例婴幼儿复杂心脏畸形的外科治疗

Surgical Treatment of Complex Congenital Heart Diseases in 57 Infants

报告１９９１年９月至１９９４年８月期间收治的５７例婴幼儿复杂先天性心脏病，包括右室双出口１６例、完全性大动脉转位８例、完全性心内膜垫缺损７例、完全性肺静脉畸形引流６例、肺动脉闭锁４例、单心房４例、三尖瓣闭锁和主动脉弓中断各３例、左冠状动脉右室瘘２例、单心室和镰刀综合征各１例及其他复杂畸形２例。６例行姑息性手术，手术早期死亡１例（１６．７％）；５１例行一期矫治术，手术早期死亡９例（１７．６％）。总手术早期死亡为１７．５％，最近２年早期死亡率为１２．５％。主要死亡原因为肾功能衰竭和低心输出量综合征。

To summarize the expeirence of surgical treatment of complex congenital heast diseases.Between September,1991 and August 1994.57 infants with complex congenital heart diseases incliuding 16 cases of double outlet right ventricle 8 complete transposition of great arteries,7 complete atrioventricular canal defects,6 total anomalous pulmonary venous connections 4 pulmonary atreesia,tricuspid atresia and 3 aortic arch interruption 2 left coronary artery right ventricle fistula,1 single ventricle,1 sickle cell syndrome and 2 other complex anomalies,were operated upon at Fuwai Hospital.Palliative procedures were performed on 6 patients with one in hospital death(16.7%) and corrective operations on 51 with 9 in hospital deaths (17.6%).The over all postoperative mortality was 17.5% and was reduced to 12.5% in recent 2 years.The main causes of deaths were low cardiac output syndrome and kidney failure.