眼睑松弛综合征

Blepharochalasis syndrome

眼睑松弛综合征是一种少见眼睑疾病,以青少年反复发作性眼睑水肿为特征。可并发泪腺脱垂、上睑下垂和睑裂横径缩短等。发病机制可能与自身免疫反应弹性纤维丢失有关。诊断方面需注意与多发生于青年人中的双侧上睑肿胀疾病进行鉴别。治疗以上睑成形术为首选,手术时机应选择病情静止1a以上进行。

Blepharochalasis syndrome is an uncommon eyelid disorder characterized by recurrent episodes of eyelid edema in young patients. Many patients develop blepharochalasis, prolapse of the lacrimal gland and horizontally shortened palpebral fissure. Pathogenesis of this disease is probably immunological with nearly complete loss of elastic fibers. The differential diagnosis should give special attention to diseases with bilateral upper eyelid turgescence in young people. Blepharoplasty remains the primary treatment, which should be deferred for at least one year from the previous attack of eyelid edema.