选择性多脑叶切除联合致痫皮层热灼术治疗Sturge-weber综合征1例

One case of Selective multi-lobectomy combining with bipolar coagulation in Sturge-Weber syndrome

目的探讨多脑叶切除治疗Sturge-weber综合征。方法结合国内外文献,分析1例采用右额颞顶枕开颅选择性多脑叶切除联合致痫皮层热灼术治疗Sturge-weber综合征。结果术后随访6个月有一次癫痫小发作,无功能障碍。结论Sturge-weber综合征药物治疗无效,手术治疗是唯一有效的方法。大脑半球切除术最为有效,但并非所有类型的都适合,有的病例导致严重的功能障碍。我科首例行选择性多脑叶切除+致痫皮层热灼术,效果满意。

Objective To explore the effectiveness of multi-lobectomy in Sturge-Weber syndrome. Methods To analysis one Sturge-Weber case by searching relevant literatures, in which we treated by combining right fronto-temp to-parietal-occipital craniotomy selective multi-lobectomy with bipolar coagulation. Results After 6- month follow-up, the patient had one pit mal seizure, with no function lose. Conclusion Surgical therapy is the only effective treatment for the Sturge-Weber syndrome. , and drug treatment shows no use. Athough hemi-spherectomy is the most valuable therapy, it isn＇t fit to all kinds of Sturge-Weber syndrome cases. Some patients will suffer serous function deficients from hemispherectomy. For such kind of patients, we chose the selective multi-lobectomy combining with bipolar coagulation technique to treat them and acquire excellent results firstly in China.