双侧听神经瘤
摘要
神经纤维瘤病2型（neurofibromatosis type2，NF2）是一种常染色体显性遗传病，临床表现多样，双侧听神经瘤为其典型表现。NF2根据临床表现分为三型：Ⅰ型为Wishart型：多在青少年时期发病，临床症状最严重，除了表现为双侧听神经瘤以外，患者往往还罹患多发颅内和脊柱肿瘤；Ⅱ型为Gardner型：发病较晚，症状较轻，颅内肿瘤少见；Ⅲ型为嵌合体型（Mosaicism）：
出处
《中华耳鼻咽喉头颈外科杂志》
CAS
CSCD
北大核心
2008年第3期237-240,共4页
Chinese Journal of Otorhinolaryngology Head and Neck Surgery
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