少汗型外胚层发育不良症的临床特点及义齿修复

Clinical features and prosthodontics of hypohydrotic ectodermal dysplasia

少汗型外胚层发育不良症是一类相对常见的遗传性综合性疾病,先天性牙缺失是此类疾病的主要口腔表现。少汗型外胚层发育不良症患者通常就诊年龄较小,颌骨发育尚未完全,且常伴有牙槽突发育不良,故其义齿修复具有特殊性,对其进行"序列治疗"的观点也应运而生。本文就少汗型外胚层发育不良症的临床特点以及义齿修复作一综述。

Hypohydrotic ectodermal dysplasia is a common group of hereditary diseases, with congenital tooth loss as the predominant oral symptom. The prosthodontics of hypohydrotic ectodermal dysplasia is special because most of the affected patients are pre-adolescents, whose jaw bones and alveolar process are lack of development. A sequence treatment option is applied in the treatment procedure. This review included the clinical features and prosthodontics of hypohydrotic ectodermal dysplasia, depending on large numbers of relavant literatures.