摘要
As a non-atherosclerotic chronic cerebral vasculopathy, moyamoya disease is characterized by progressivesteno-occlusion of the arteries of the circle of Willis with a developed collateral vascular network mainly at the cerebral base. And it is named moyamoya disease because of a characteristic ＂puff-of-smoke＂ angiographic appearance. The steno-occlusive process is typically seen involving bilateral internal carotid arteries at their clinoid portion and/or the proximal portion of the anterior cerebral arteries （ACAs） and/or the middle cerebral arteries （MCAs）. The coexistence of moyamoya disease and arteriovenous malformation （AVM） is thought to be very rare.
As a non-atherosclerotic chronic cerebral vasculopathy, moyamoya disease is characterized by progressivesteno-occlusion of the arteries of the circle of Willis with a developed collateral vascular network mainly at the cerebral base. And it is named moyamoya disease because of a characteristic ＂puff-of-smoke＂ angiographic appearance. The steno-occlusive process is typically seen involving bilateral internal carotid arteries at their clinoid portion and/or the proximal portion of the anterior cerebral arteries （ACAs） and/or the middle cerebral arteries （MCAs）. The coexistence of moyamoya disease and arteriovenous malformation （AVM） is thought to be very rare.
