以反复喘息为表现的肺动脉吊带畸形2例报告并文献复习

Pulmonary artery sling:two cases report and literature review

目的提高对肺动脉吊带畸形(PAS)的认识和早期诊疗水平,减少漏诊、误诊。方法分析2例婴幼儿PAS的临床资料,评价超声心动图、支气管镜、螺旋CT、MRI等方法在早期诊断方面的作用。结果2例患儿主要临床表现为反复喘息、肺部感染。初次发病年龄<3个月,且多次住院,纤支镜检查示气管狭窄,1例经螺旋CT及超声心动图确诊,1例经手术诊断。结论婴儿早期出现反复喘息、肺部感染及气道梗阻表现时,应考虑PAS可能。超声心动图、螺旋CT、MRI是确诊的最佳方法。

Objectives To raise awareness of pulmonary artery sling （PAS） and to improve its early diagnosis and reduce misdiagnosis. Methods The information of two cases were analyzed and evaluation of echocardiography, bronchoscopy, spiral CT and MRI methods for early diagnosis were performed. Results These two children had major clinical manifestations of recurring wheezing and pneumonia, initial age of onset 〈 3 months, and repeated hospitalization. Rronchoscopy examination revealed tracheal stenosis. One case was confirmed by spiral CT and echocardiography, and one case was confirmed by surgery to have PAS. Conclusions Repeatedly wheezing, lung infection and airway obstruction manifestations in early infancy should consider PAS. Echocardiography, spiral CT, and MRI is the best methods to the diagnosis of PAS.