小儿特发性肺含铁血黄素沉着症32例分析

Idiopathic Pulmonary Hemosiderosis in Children Xu Youhua Zhang Rongjun

小儿特发性肺含铁血黄素沉着症是呼吸道的一种少见疾病。本文总结了1991年～1996年住院的32例特发性肺含铁血黄素沉着症。本组临床资料特点：年龄＜10岁而具有反复呼吸道感染伴不明原因缺性贫血，不明原因间歇咯血，气促，肺部体征与临床表现及胸对改变不一致性，查疫及胃液中找到合铁血黄素吞噬细胞，除外继发性肺含铁血黄素沉着症，结合文献提出本病诊断要点及处理原刚；探讨病因及总结了造成误诊原因，以期提高对本病的早期诊断治疗，改善预后，提高生存率。

Idiopathic pulmonary hemosiderosis is a very few pulmonary disease in children. Thirty two cases treated in the inpatient department of our hospital from 1991 to 1996 were reported in this paper, Clinical chararteristics of this group patient showed folow :①All patients aged under ten years. ②Recured pulmonary infection and unknow-cause iron deficiency anemia and interval hemoptysis and shortness of breath. ③There were unidentical between the sings of lung and clinical symptoms and lung damagc showed on the X-ray plan. ④phagocytes with hemosiderin were faund in the phegm and gastric juice of the patlents. Principics of diagnosis and treatment were discussed in this paper for improving prognosis.