摘要
Introduction Epithelioid hemangioendothelioma(EHE)is an uncommon vascular tumor,which also has been called histiocytoid haemangioma.This low-grade malignant tumor was first described as a distinctive entity in 1982 by Weiss and Enzinger.Histopathologically,EHE is charac- terized by round or spindle-shaped endothelial cells with
Epithelioid hemangioendothelioma (EHE) is an uncommon vascular tumor, which also has been called histiocytoid haemangioma. This low-grade malignant tumor was first described as a distinctive entity in 1982 by Weiss and Enzinger Histopathologically, EHE is characterized by round or spindle-shaped endothelial cells with cytoplasmic vacuolation121. The tumor may occur in numerous organs, including liver, lung, parotid grand, skin, pleura, thyroid, spleen, cardiac valve, radial artery, oral cavity and parapharyngeal space. Many cases have been reported, but its etiology and natural history remain unclear.