2Furlan M,Robles R,Lamie B.Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis.Blood,1996,87:4223-4234.
3Tsai HM.Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion.Blood,1996,87:4235-4244.
4Zheng X,Chung D,Takayama TK,et al.Structure of von Willebrand factor-cleaving protease (ADAMTS13),a metalloprotease involved in thrombotic thrombocytopenic purpura.J Biol Chem,2001,276:41059-41063.
5Fujikawa K,Suzuki H,McMullen B,et al.Purification of human von Willebrand factor-cleaving protease and its identification as a new member of the metalloproteinase family.Blood ,2001,98:1662-1666.
6Rick ME,Molls S,Taylor MA.Clinical use of a rapid collagen binding assay for yon Willebrand factor cleaving protease in patients with thrombotic thrombocytopenic purpura.Thromb Haemost,2002,88:598-604.
7Furlan M,Robles R,Solenthaler M ,et al.Acquired deficiency of von Willebrand factor-cleaving protease in a patient with thrombotic thrombocytopenic purpura.Blood,1998,91:2839-2846.
8Tsai HM,Lian EC.Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura.N Engl J Med,1998,339:1585-1594.
9Zheng XL,Kaufman RM,Goodnough LT,et al.Effect of plasma exchange on plasma ADAMTS13 metalloprotease activity,inhibitor level,and clinical outcome in patients with idiopathic and nonidiopathic thrombotic thrombocytopenic purpura.Blood,2004,103:4043-4049.
10George JN,Vesely SK,Terrell DR.The Oklahoma Thrombotic Thrombocytopenic Purpura-Hemolytic Uremic Syndrome (TTPHUS) Registry:a community perspective of patients with clinically diagnosed TTP-HUS.Semin Hematol,2004 ,41:60-67.