复发性多软骨炎的诊断及治疗(附1例报告)

The diagnosis and treatment of relapsing polychondritis(a case report)

目的:提高对复发性多软骨炎的诊断及治疗水平。方法:报道1例37岁女性患者的临床资料,并进行相关文献复习。结果:患者首发症状为双侧耳廓软骨炎,首诊拟诊为右侧突发性聋,治愈出院2个月后,再发双侧耳廓软骨炎并伴心脏、眼等器官受累,确诊为复发性多软骨炎。结论:复发性多软骨炎是少见的自身免疫性疾病,早期临床表现不典型,易误诊、漏诊。经皮质激素、免疫抑制剂、氨苯砜治疗或手术可控制症状。

Objective：To enhance the understanding of the diagnosis and treatments of relapsing polychondritis （RP）. Method： We present a 37 years old woman With RP, and review the literatures. Result： Initial presenting symptoms of the patient was auricle perichondritis. The patient was diagnosed as sudden deafness firstly. After 2 months, she consulted otolaryngologists at second time with a variety of involvement of the ear, nose, larynx or heart. She was diagnosed as relapsing polychondritis finally. Conclusion：RP was rare autoimmune system disease, early clinical manifestation were atypical, misdiagnosis and diagnostic errors usually occurred. Corticosteroids, immunosuppressive agents, dapsone and surgical operation could be used in these patients to control symptoms.