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超声心动图对肺动脉闭锁伴室间隔缺损的诊断价值

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摘要 肺动脉闭锁伴室间隔缺损(PA/VSD)是少见的严重紫绀型先天性心脏性(简称先心病),本病以往报道其出生后1年病死率高达70%。其主要病理特点是肺动脉瓣、右室漏斗部或肺动脉主干直立分叉部完全闭锁,肺动脉系统的血供主要依靠未闭的动脉导管和/或体一肺动脉侧支血管供应。现将本院经超声检出12例PA/VSD的结果报道如下。
出处 《浙江医学》 CAS 2008年第10期1138-1139,共2页 Zhejiang Medical Journal
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参考文献4

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