摘要
本文报告法乐四联症肺小动脉病变的定量分析及其临床特征。结果显示，四联症肺小动脉中层随年龄增长至进行性废用性萎缩，其中层厚度与左右肺动脉干的发育、在心功能相关。中层严重萎缩者术后易发生低心排综合症，特别是低年龄中层萎缩者。作者认为，四联症肺小动脉病变与低肺血流量有关，因此四联症宜早期手术，恢复正常的肺血流量，以利于肺小动脉的正常演变。
This paper reports the quantitative analysis of pulmonary arteriole disease of the tetralogy ofFallot,and it's clinical characteristics. The result showed that the medium at pulmonary arteriolein tetralogy of Fallot atrophy progressed with increasing age. The thickness of medium was related to the development of pulmonary artery trunk and to the functiQn of the left ventricular. Theserious atrophy in media predisposed the occurrence of postoperative low cardiac output. This datasuggested that the pulmonary vascular disease in tetralogy of Fallot was related to the diminishedpulm0nary blood flow. There fore,the tetralogy of Fallot should be treated surgically early to protect the development of pulmonary vessels.
