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遗传性联合凝血因子Ⅴ与Ⅷ缺乏症1例报告

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摘要 遗传性联合凝血因子缺乏症是一组罕见的出血性疾病。该文报道1例遗传性凝血因子Ⅴ联合因子Ⅷ缺乏症,主要临床表现为自幼起牙龈间断渗血;实验室检查血浆凝血因子Ⅴ凝血活性部分(factor Ⅴ coagulant activity,FⅤ∶C)、FⅧ:C异常,抗FⅤ∶C与FⅧ∶C抗体正常。提示对于自发性出血患者,在排除继发因素后应尽快转送上级医院检查以明确有否凝血因子缺乏。
出处 《新医学》 2009年第2期111-112,共2页 Journal of New Medicine
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