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致心律失常性右心室心肌病

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摘要 致心律失常性右心室心肌病（arrhythmogenic right ventricular cardiomyopathy，ARVC）亦称致心律失常性右心室发育不良，是一种以右心室的结构和功能异常为特点的心肌病变，心肌细胞被脂肪和纤维组织所取代，有一定家族倾向，是年轻人和运动员猝死的主要病因。在30岁以下的猝死患者中，ARVC可占20％。有报道称ARVC发病率约为1／5000，由于存在漏诊、误诊，可能实际发病率要高一些。
作者 陈颖莹 毛家亮
机构地区 上海交通大学医学院附属仁济医院心内科
出处 《中国综合临床》 2009年第3期228-230,共3页 Clinical Medicine of China
关键词 致心律失常性右心室心肌病 遗传学 诊断 治疗
分类号 R542.2 [医药卫生—心血管疾病] R587.2 [医药卫生—内分泌]
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参考文献23

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二级参考文献93

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中国综合临床
2009年 第3期

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