伴毛囊黏蛋白沉积的向毛囊性蕈样肉芽肿

Folliculotropic mycosis fungoides with follicular mucinosis:a report of two cases

报告2例伴有毛囊黏蛋白沉积的向毛囊性蕈样肉芽肿。例1.女,39岁。面部、躯干、四肢出现红斑、丘疹,伴瘙痒3年余就诊。例2.男,52岁。躯干、四肢出现红斑、斑块1年就诊;结合组织病理检查、免疫组化染色及淋巴细胞克隆性基因重排检测,2例患者均诊断为伴有毛囊黏蛋白沉积的向毛囊性蕈样肉芽肿。

Two cases of folliculotropic mycosis fungoides with follicular mucinosis are reported. A 39-year-old woman presented with erythema and papules on the face, trunk and limbs accompanied by itching for 3 years. Another 52-year-old man presented with a history of more than 1-year of erythema and plaques on the trunk and limbs. Both were diagnosed as folliculotropic mycosis fungoides with follicular mucinosis, according to the histopathology of the skin specimen, the immunohistochemical study and a study of T-cell receptor gene rearrangement.