73例单心室临床观察

Clinical features of single ventricle in 73 cases

目的单心室临床表现颇复杂，为提高临床诊断准确率，我们分析７３例单心室的临床特征。方法分析７３例单心室的心电图、超声心动图、心血管造影和手术所见，以探讨临床特征与形态学关系。结果７３例中，Ａ型单心室６１例，Ｂ型４例，Ｃ型８例；６例单心室并单心房，其中５例并心脏异位；６１例存在房间交通；５８例有二组房室瓣；１５例为一组房室瓣；７１例存在多处肺动脉狭窄。结论单心室易并存多种心内畸形及心脏异位，手术前仔细观察心内各部位结构，有利于诊断和手术方式的选择。

Objective Single ventricle (SV) appears complex on clinical features. Clinical features in 73 cases of SV were studied in order to improve the diagnosis of SV.Methods Electrocardiogram, ultrasound cardiograph, cardioangiograph and operative finding in 73 cases of SV were analyzed.Results Sixty one cases were of type A, 4 of type B and 8 of type C. No case of type D was found in this series. Five of the 6 cases of SV with single atrium were complicated by malposition of the heart. Atrial communications were present in 61 cases. Double atrioventricular valves were detected in 58 cases and single atrioventricular valve in 15 cases. Multiple pulmonary stenoses were present in 71 cases. Conclusion SV is frequently associated with other intracardiac malformation and malposition so a careful preoperative study on the intracardiac structures is very helpful for the diagnosis and operation.