肠气囊肿病及内科治疗进展

肠气囊肿病(Pneumatosis Cystoides Intestinalis,PCI)是一少见疾病.其特征是发生于胃肠道任何部位的粘膜下、浆膜下或肠系膜多发性气性囊肿.在成人,PCI通常被看作良性疾病,常与胃肠道和呼吸器官疾病有关、婴儿肠气囊肿病与肠坏死有关,病情严重,病死率很高.该病命名较多、如小肠气囊病(gas cysts of the in testine),腹膜气囊肿病(peritoneal pneumatosis.肠气肿(interstinal emphysema)·囊性淋巴气囊肿炳(cystic lylphopneumatosis),小肠球状囊肿病(bullous emphysema of the intestine ),腹腔肠气肿(imtestitial ab dominal emphysema),目前统一将该病命名为肠气囊肿病(PCI).