巨大脊髓圆锥血管母细胞瘤一例并文献复习

Large hemangioblastoma of the conus medullaris ： a case report and review of the literature

目的探讨脊髓血管母细胞瘤的诊断、治疗及预后。方法对1例圆锥部位巨大血管母细胞瘤的诊治进行报告，并结合文献对脊髓血管母细胞瘤进行回顾分析。结果脊髓血管母细胞瘤可以是单独发生，也叮以是Von Hippel—Lindau病的系列疾病之一，临床发病率低，最常见症状是疼痛，MRI表现为瘤结节明显强化，周围可见异常血管流空影，多伴有空洞，DSA可显示染色的瘤结节、供血动脉及引流静脉，显微神经外科手术可完整全切。结论显微神经外科手术是治疗脊髓血管母细胞瘤的最佳方法。对于有症状患者，应尽早手术，无症状患者可以定期复查MRI，如表现为肿物生长，可视为手术指证，患者预后较好。

Objective To discuss the diagnosis, treatment and prognosis of spinal hemangioblastoma. Methods One large conus medullaris hemangioblastoma was reported, and the related literature was reviewed. Results Spinal Hemangioblastomas are rare vascular tumors, which can occur as sporadic or as component tumor of von Hippel - Lindau disease. MRI and DSA can help to diagnose the spinal Hemangioblastoma that can be totally reseeted by micro -neurosurgery. Conclusion The total microsurgical resection of the tumor is the best treatment and can attain good prognosis.