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Kasabach—Merritt综合征并发严重凝血障碍一例 被引量:1

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摘要 患者女,13岁。因颈部巨大血管瘤合并出血2周于2008年3月26日急诊入院。患儿出生时左上肢即有青紫样斑块,随生长逐渐增大,波及左上肢、胸背及颈部。瘤体呈压缩、非搏动囊性包块,部分皮色青紫(图1)。Valsalva动作可致包块增大,瘤内可触及黄豆大小静脉石。CT示脾脏巨大血管瘤(图2)。颈前部血管瘤见皮肤缝线及2cm破溃面。近半年瘤体不明原因迅速增大。
出处 《中华普通外科杂志》 CSCD 北大核心 2009年第8期616-616,共1页 Chinese Journal of General Surgery
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参考文献1

  • 1Michael N. Kasabach-Merritt syndrome : dangers of interferon and successful treatment with pentoxifylline. J Pediatric Surg, 2006,41 : E29-E31.

同被引文献11

  • 1Drolet BA,Scott LA,Esterly NB,et al.Early surgical intervention in a patient with Kasabach-Merritt phenomenon.J Pediatr,2001,138(5):756-758.
  • 2Wang P,Zhou W,Tao L,et al.Clinical analysis of Kasabach-Merritt syndrome in 17 neonates.BMC Pediatr,2014,14:146.
  • 3Shen W,Cui J,Chen J,et al.Kasabach-Merritt syndrome:case reports of successful treatment with partial tumor resection and vincristine chemotherapy.Ann Plast Surg,2010,65(3):361-363.
  • 4Shin HY,Ryu KH,Ahn HS.Stepwise multimodal approach in the treatment of Kasabach-Merritt syndrome.Pediatr Int,2000,42(6):620-624.
  • 5Warrell RJ,Kempin SJ.Treatment of severe coagulopathy in the Kasabach-Merritt syndrome with aminocaproic acid and cryoprecipitate.N Engl J Med,1985,313(5):309-312.
  • 6Aslan A,Meyer Zu Vilsendorf A,Kleine M,et al.Adult Kasabach-Merritt syndrome due to hepatic giant hemangioma.Case Rep Gastroenterol,2009,3(3):306-312.
  • 7Chen CE,Ko JY,Wang CJ.Kasabach-Merritt syndrome complicating the treatment of a femoral shaft fracture in an adult.J Trauma,2002,52(4):789-792.
  • 8Yasui N,Koh K,Kato M,et al.Kasabach-Merritt phenomenon:a report of 11 cases from a single institution.J Pediatr Hematol Oncol,2013,35(7):554-558.
  • 9Hermans DJ,van Beynum IM,van der Vijver RJ,et al.Kaposiform hemangioendothelioma with Kasabach-Merritt syndrome:a new indication for propranolol treatment.J Pediatr Hematol Oncol,2011,33(4):e171-e173.
  • 10Mukhtar IA,Letts M.Hemangioma of the radius associated with Kasabach-Merritt syndrome:case report and literature review.J Pediatr Orthop,2004,24(1):87-91.

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